TY - JOUR
T1 - Adult-Onset Still's Disease with Atypical Persistent Rash and Histologic Findings of Neutrophilic Urticarial Dermatosis
AU - Park, Yu Jeong
AU - Shin, Hui Young
AU - Choi, Woo Kyoung
AU - Sim, Hyun Bo
AU - Hong, Jong Soo
AU - Lee, Ai Young
AU - Lee, Seung Ho
N1 - Publisher Copyright:
© 2024 Korean Dermatological Association. All rights reserved.
PY - 2024/1
Y1 - 2024/1
N2 - Adult-onset Still's disease (AOSD) is a rare systemic inflammatory disease characterized by spiking fever, arthralgia, skin rashes, and hyperferritinemia. The rash is usually salmon-colored, non-itchy, accompanied by fever, and disappears with an improvement of fever. However, in some cases, the rash persisted regardless of fever. Here, we present a case of AOSD with an atypical persistent rash that showed histological findings resembling those of neutrophilic urticarial dermatosis. The patient was a 60-year-old woman with high fever, arthralgia, and a persistent flagellated skin rash. Despite systemic steroid treatment, the patient developed a serious complication: macrophage activation syndrome. Since this case presented with an atypical persistent rash with histological resemblance to neutrophilic urticarial dermatosis, we report its contribution to the further study of AOSD.
AB - Adult-onset Still's disease (AOSD) is a rare systemic inflammatory disease characterized by spiking fever, arthralgia, skin rashes, and hyperferritinemia. The rash is usually salmon-colored, non-itchy, accompanied by fever, and disappears with an improvement of fever. However, in some cases, the rash persisted regardless of fever. Here, we present a case of AOSD with an atypical persistent rash that showed histological findings resembling those of neutrophilic urticarial dermatosis. The patient was a 60-year-old woman with high fever, arthralgia, and a persistent flagellated skin rash. Despite systemic steroid treatment, the patient developed a serious complication: macrophage activation syndrome. Since this case presented with an atypical persistent rash with histological resemblance to neutrophilic urticarial dermatosis, we report its contribution to the further study of AOSD.
KW - Adult-onset Still's disease
KW - Neutrophilic urticarial dermatosis
UR - http://www.scopus.com/inward/record.url?scp=85186333696&partnerID=8YFLogxK
M3 - Article
AN - SCOPUS:85186333696
SN - 0494-4739
VL - 62
SP - 42
EP - 45
JO - Korean Journal of Dermatology
JF - Korean Journal of Dermatology
IS - 1
ER -